Pyruvate dehydrogenase deficiency management | 食品添加物合法業者資訊網
ManagementofPyruvateDehydrogenaseComplexDeficiencyBasedonGeneticCause·由RGanetzky著作·2021—Primarypyruvatedehydrogenasecomplexdeficiency(PDCD)isa ...,,Dichloroacetatemaybeadministeredtotreatlacticacidosis,eitherintravenouslyduringacuteepisodesororallyonaregularbasis.Manyaffectedindividuals ...,由HPavlu-Pereira著作·2020·被引用16次—Treatment.Allthepatientsareundertherapeuticmeasureswhichincludeketogenicdiet,thiaminesupplementationandantiepilepticdrugs.Three ...,2018年8月17日—Directtreatmenttha...
Primary Pyruvate Dehydrogenase Complex Deficiency Overview | 食品添加物合法業者資訊網
Pyruvate dehydrogenase complex deficiency | 食品添加物合法業者資訊網
Pyruvate Dehydrogenase Complex Deficiency | 食品添加物合法業者資訊網
Pyruvate dehydrogenase complex deficiency | 食品添加物合法業者資訊網
Pyruvate Dehydrogenase Deficiency (PDCD) Treatment ... | 食品添加物合法業者資訊網
Pyruvate dehydrogenase deficiency | 食品添加物合法業者資訊網
Pyruvate dehydrogenase deficiency | 食品添加物合法業者資訊網
【鹽酸硫胺明(維生素B1) 50189】食品添加物產品登錄碼:TFAA20000133373
添加物名稱:鹽酸硫胺明(維生素B1)50189;食品添加物產品登錄碼:TFAA20000133373食品業者登錄字號:A-128185154-00000-2添加物...
【鹽酸硫胺明 (維生素B1,鹽酸色噻胺)】食品添加物產品登錄碼:TFAA1N003063007
添加物名稱:鹽酸硫胺明(維生素B1,鹽酸色噻胺);ThiamineHydrochloride(VitaminB1)食品添加物產品登錄碼:TFAA1N003063007食品...
【鹽酸硫胺明 (維生素B1,鹽酸色噻胺)】食品添加物產品登錄碼:TFAB1M012856007
添加物名稱:鹽酸硫胺明(維生素B1,鹽酸色噻胺);ThiamineHydrochloride(VitaminB1)食品添加物產品登錄碼:TFAB1M012856007食品...
【硝酸硫胺明 (維生素B1,硝酸噻胺)】食品添加物產品登錄碼:TFAB1M012879002
添加物名稱:硝酸硫胺明(維生素B1,硝酸噻胺);ThiamineMononitrate(VitaminB1)(ThiamineNitrate)食品添加物產品登錄碼:TFAB1M...
【乙醯乳酸脫羧酶】食品添加物產品登錄碼:TFAB20000059528
添加物名稱:乙醯乳酸脫羧酶;MaturexPro(ALDC)食品添加物產品登錄碼:TFAB20000059528食品業者登錄字號:A-114012061-00000-3添...
【噻唑】食品添加物產品登錄碼:TFAB30000264954
添加物名稱:噻唑;Thiazole食品添加物產品登錄碼:TFAB30000264954食品業者登錄字號:H-122868808-00000-7添加物分類:型態:液狀...
【鹽酸硫胺明 (維生素B1,鹽酸色噻胺)】食品添加物產品登錄碼:TFAB1M012878001
添加物名稱:鹽酸硫胺明(維生素B1,鹽酸色噻胺);ThiamineHydrochloride(VitaminB1)食品添加物產品登錄碼:TFAB1M012878001食品...
【丙酮酸】食品添加物產品登錄碼:TFAB30000138033
添加物名稱:丙酮酸;PyruvicAcid,Synthetic食品添加物產品登錄碼:TFAB30000138033食品業者登錄字號:B-189377675-00000-1添加...
【硝酸硫胺明(維生素B1,硝酸噻胺)】食品添加物產品登錄碼:TFAB1C008270002
添加物名稱:硝酸硫胺明(維生素B1,硝酸噻胺);THIAMINEMONONITRATE(VITAMINB1)食品添加物產品登錄碼:TFAB1C008270002食品業者...
【丙酮酸】食品添加物產品登錄碼:TFAB30000233264
添加物名稱:丙酮酸;PyruvicAcid食品添加物產品登錄碼:TFAB30000233264食品業者登錄字號:N-128151176-00000-2添加物分類:型態...
【苯并噻唑】食品添加物產品登錄碼:TFAB30000281829
添加物名稱:苯并噻唑;Benzothiazole食品添加物產品登錄碼:TFAB30000281829食品業者登錄字號:F-116894172-00000-1添加物分類:...
【鹽酸硫胺明 (維生素 B1)】食品添加物產品登錄碼:TFAA1D001694005
添加物名稱:鹽酸硫胺明(維生素B1);THIAMINEHYDROCHLORIDE(VITAMINB1)食品添加物產品登錄碼:TFAA1D001694005食品業者登錄字號...
【硝酸硫胺明 (維生素B1,硝酸噻胺)】食品添加物產品登錄碼:TFAB1M012857008
添加物名稱:硝酸硫胺明(維生素B1,硝酸噻胺);ThiamineMononitrate(VitaminB1)食品添加物產品登錄碼:TFAB1M012857008食品業者...
【丙酮酸】食品添加物產品登錄碼:TFAA30000626269
添加物名稱:丙酮酸;PYRUVICACID食品添加物產品登錄碼:TFAA30000626269食品業者登錄字號:H-122868808-00000-7添加物分類:型態...
【鹽酸硫胺明 (維生素B1,鹽酸色噻胺)】食品添加物產品登錄碼:TFAB1M013025006
添加物名稱:鹽酸硫胺明(維生素B1,鹽酸色噻胺);ThiamineHydrochloride(VitaminB1)食品添加物產品登錄碼:TFAB1M013025006食品...