Pyruvate Dehydrogenase Complex Deficiency | 食品添加物合法業者資訊網
Dichloroacetatemaybeadministeredtotreatlacticacidosis,eitherintravenouslyduringacuteepisodesororallyonaregularbasis.Manyaffectedindividuals ...
Last updated: June 14, 2021 Years published: 1987, 1988, 1990, 1992, 1994, 1998, 1999, 2004, 2007, 2010, 2021
Disease OverviewPyruvate dehydrogenase complex deficiency (PDCD) is a rare disorder of carbohydrate metabolism caused by a deficiency of one of the three enzymes in the pyruvate dehydrogenase complex (PDC). The age of onset and severity of disease symptoms vary widely. Individuals with PDCD symptom onset in the prenatal period or in infancy usually die in early childhood. Those who develop PDCD later in childhood may have neurological symptoms but usually survive into adulthood. Most individuals with PDCD have an abnormality in the PDHA1 gene located on the X chromosome. A smaller percentage of affected individuals have forms of the disorder that follow autosomal recessive inheritance.
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Pyruvate dehydrogenase complex deficiency | 食品添加物合法業者資訊網
Pyruvate Dehydrogenase Complex Deficiency | 食品添加物合法業者資訊網
Pyruvate dehydrogenase complex deficiency | 食品添加物合法業者資訊網
Pyruvate Dehydrogenase Deficiency (PDCD) Treatment ... | 食品添加物合法業者資訊網
Pyruvate dehydrogenase deficiency | 食品添加物合法業者資訊網
Pyruvate dehydrogenase deficiency | 食品添加物合法業者資訊網
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