0326 丙酮酸鹽脫氫酶缺乏症Pyruvate Dehydrogenase | 食品添加物合法業者資訊網

Pyruvate dehydrogenase is an enzyme that catalyzes the reaction of pyruvate and a lipoamide to give the acetylated dihydrolipoamide and carbon dioxide. Read More

丙酮酸脫氫酶複合體（英語：Pyruvate dehydrogenase complex；PDH complex；PDC；也称为丙酮酸去氫酶複合物）是生物體內催化丙酮酸轉變成乙醘輔酶A之反應的三種酶及五 ... Read More

Pyruvate dehydrogenase (PDH) is a convergence point in the regulation of the metabolic finetuning between glucose and FA oxidation. Hence, PDH converts pyruvate ... Read More

2012年7月1日 — Pyruvate dehydrogenase deficiency is characterized by the buildup of a chemical called lactic acid in the body and a variety of neurological ... Read More

由 G Sutendra 著作 · 2013 · 被引用 241 次 — Pyruvate dehydrogenase kinase (PDK) is a mitochondrial enzyme that is activated in a variety of cancers and results in the selective ... Read More

病因學： 此症的致病原因是因為由於人體內丙酮酸鹽脫氫酶（Pyruvate dehydrogenase；E1）缺乏，在兒童期的患童大多數會引發原發性的乳酸中毒（primary lactic acidosis）。 Read More