Maple syrup urine disease genereviews | 食品添加物合法業者資訊網
248600-MAPLESYRUPURINEDISEASE;MSUD-BRANCHED-CHAINKETOACIDURIA;;BRANCHED-CHAINALPHA-KETOACIDDEHYDROGENASEDEFICIENCY;;BCKDDEFICIENCY;; ...,由KAStrauss著作·2020·被引用194次—Maplesyrupurinedisease(MSUD)iscausedbydecreasedactivityofthebranched-chainalpha-ketoaciddehydrogenasecomplex(BCKD),thesecond ...,Maplesyrupurinedisease(MSUD)isararegeneticdisordercharacterizedbydeficiencyofanenzymecomplex(branched-chainalpha-ketoaciddehydrogenase) ...,由KAStrauss著作·1993·被引用194次—Geneticcounseling:MSUDis...
248600 | 食品添加物合法業者資訊網
Maple Syrup Urine Disease | 食品添加物合法業者資訊網
Maple Syrup Urine Disease | 食品添加物合法業者資訊網
Maple Syrup Urine Disease | 食品添加物合法業者資訊網
Maple syrup urine disease | 食品添加物合法業者資訊網
【楓糖香基 T-02-E-5】食品添加物產品登錄碼:TFAA30000649219
添加物名稱:楓糖香基T-02-E-5;MAPLEBASET-02-E-5食品添加物產品登錄碼:TFAA30000649219食品業者登錄字號:H-122868808-00000-...
【楓糖香基 T-02-E-50】食品添加物產品登錄碼:TFAA30000201831
添加物名稱:楓糖香基T-02-E-50;MAPLEBASET-02-E-50食品添加物產品登錄碼:TFAA30000201831食品業者登錄字號:H-122868808-0000...
【楓糖香料SF-110003-1】食品添加物產品登錄碼:TFAA30000464696
添加物名稱:楓糖香料SF-110003-1;MAPLESUGARFLAVOUR食品添加物產品登錄碼:TFAA30000464696食品業者登錄字號:N-116876554-000...
【楓糖香料 C-4235】食品添加物產品登錄碼:TFAA30000063646
添加物名稱:楓糖香料C-4235;MapleFlavorC-4235食品添加物產品登錄碼:TFAA30000063646食品業者登錄字號:F-103049203-00000-4...
【MAPLE FLAVOR KW-2536】食品添加物產品登錄碼:TFAA30000569131
添加物名稱:MAPLEFLAVORKW-2536;食品添加物產品登錄碼:TFAA30000569131食品業者登錄字號:J-180716148-00000-2添加物分類:楓...