Leigh Syndrome | 食品添加物合法業者資訊網
Leighsyndromeisararegeneticneurometabolicdisorder.Itischaracterizedbythedegenerationofthecentralnervoussystem(i.e.,brain,spinalcord, ...
Disease OverviewLeigh syndrome is a rare genetic neurometabolic disorder. It is characterized by the degeneration of the central nervous system (i.e., brain, spinal cord, and optic nerve). The symptoms of Leigh syndrome usually begin between the ages of three months and two years, but some patients do not exhibit signs and symptoms until several years later. Symptoms are associated with progressive neurological deterioration and may include loss of previously acquired motor skills, loss of appetite, vomiting, irritability, and/or seizure activity. As Leigh syndrome progresses, symptoms may also include generalized weakness, lack of muscle tone (hypotonia), and episodes of lactic acidosis, which may lead to impairment of respiratory and kidney function. Several different genetically determined enzyme defects can cause the syndrome, initially described over 60 years ago....
Leigh syndrome | 食品添加物合法業者資訊網
Leigh syndrome | 食品添加物合法業者資訊網
Leigh Syndrome | 食品添加物合法業者資訊網
Leigh syndrome | 食品添加物合法業者資訊網
Leigh syndrome | 食品添加物合法業者資訊網
Leigh syndrome | 食品添加物合法業者資訊網
Leigh syndrome | 食品添加物合法業者資訊網
Leigh's Disease | 食品添加物合法業者資訊網
The genetics of Leigh syndrome and its implications for ... | 食品添加物合法業者資訊網
【第一紅色素 C】食品添加物產品登錄碼:TFAB2C002480000
添加物名稱:第一紅色素C;DAIICHICOLORREDPOWDERC食品添加物產品登錄碼:TFAB2C002480000食品業者登錄字號:F-115013427-00000...
【丙酮酸】食品添加物產品登錄碼:TFAB30000181019
添加物名稱:丙酮酸;PYRUVICACID/2-OXOPROPIONICACID食品添加物產品登錄碼:TFAB30000181019食品業者登錄字號:F-138443032-000...
【丙酮酸】食品添加物產品登錄碼:TFAB30000174785
添加物名稱:丙酮酸;PYRUVICACID食品添加物產品登錄碼:TFAB30000174785食品業者登錄字號:A-115490309-00000-9添加物分類:型態...
【TK1】食品添加物產品登錄碼:TFAA20000097350
添加物名稱:TK1;TK1食品添加物產品登錄碼:TFAA20000097350食品業者登錄字號:A-124956270-00000-3添加物分類:粘稠劑型態:粉狀...
【丙酮酸】食品添加物產品登錄碼:TFAB30000233264
添加物名稱:丙酮酸;PyruvicAcid食品添加物產品登錄碼:TFAB30000233264食品業者登錄字號:N-128151176-00000-2添加物分類:型態...
【乙醯乳酸脫羧酶】食品添加物產品登錄碼:TFAB20000059528
添加物名稱:乙醯乳酸脫羧酶;MaturexPro(ALDC)食品添加物產品登錄碼:TFAB20000059528食品業者登錄字號:A-114012061-00000-3添...
【丙酮酸】食品添加物產品登錄碼:TFAB30000076023
添加物名稱:丙酮酸;Pyruvicacid食品添加物產品登錄碼:TFAB30000076023食品業者登錄字號:H-122868808-00000-7添加物分類:型態...
【丙酮酸】食品添加物產品登錄碼:TFAA30000626269
添加物名稱:丙酮酸;PYRUVICACID食品添加物產品登錄碼:TFAA30000626269食品業者登錄字號:H-122868808-00000-7添加物分類:型態...
【檸檬香基 K-11-3A-TF】食品添加物產品登錄碼:TFAA30000457991
添加物名稱:檸檬香基K-11-3A-TF;LEMONBASEK-11-3A-TF食品添加物產品登錄碼:TFAA30000457991食品業者登錄字號:H-122868808-00...
【甲基乙醯基原醇】食品添加物產品登錄碼:TFAB30000274999
添加物名稱:甲基乙醯基原醇;Acetylmethylcarbinol食品添加物產品登錄碼:TFAB30000274999食品業者登錄字號:H-122868808-00000...
【丙酮酸】食品添加物產品登錄碼:TFAB30000138033
添加物名稱:丙酮酸;PyruvicAcid,Synthetic食品添加物產品登錄碼:TFAB30000138033食品業者登錄字號:B-189377675-00000-1添加...