NM_000284.4(PDHA1):c.1142 | 食品添加物合法業者資訊網
![NM_000284.4(PDHA1):c.1142](https://i.imgur.com/xOaDO5F.jpg)
TheduplicationcausesaframeshiftstartingwithcodonTryptophan383,changesthisaminoacidtoaSerineresidueandcreatesaprematureStopcodonat ...
![NM_000284.4(PDHA1):c.1142](https://i.imgur.com/xOaDO5F.jpg)
This date represents the last time this VCV record was updated. The update may be due to an update to one of the included submitted records (SCVs), or due to an update that ClinVar made to the variant such as adding HGVS expressions or a rs number. So this date may be different from the date of the “most recent submission” reported at the top of this page.
Difficulties in recognition of pyruvate dehydrogenase complex ... | 食品添加物合法業者資訊網
Mild phenotype in a male with pyruvate dehydrogenase ... | 食品添加物合法業者資訊網
NM_000284.4(PDHA1):c.1142 | 食品添加物合法業者資訊網
PDHA1 gene | 食品添加物合法業者資訊網
Pyruvate dehydrogenase E1 | 食品添加物合法業者資訊網
PYRUVATE DEHYDROGENASE, ALPHA | 食品添加物合法業者資訊網
![](https://i.imgur.com/xOaDO5F.jpg)
【丙酮酸】食品添加物產品登錄碼:TFAB30000181019
添加物名稱:丙酮酸;PYRUVICACID/2-OXOPROPIONICACID食品添加物產品登錄碼:TFAB30000181019食品業者登錄字號:F-138443032-000...
![](https://i.imgur.com/xOaDO5F.jpg)
【鹽酸硫胺明 (維生素 B1)】食品添加物產品登錄碼:TFAA1D001694005
添加物名稱:鹽酸硫胺明(維生素B1);THIAMINEHYDROCHLORIDE(VITAMINB1)食品添加物產品登錄碼:TFAA1D001694005食品業者登錄字號...
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【硝酸硫胺明】食品添加物產品登錄碼:TFAB1C009266008
添加物名稱:硝酸硫胺明;THIAMINEMONONITRATE食品添加物產品登錄碼:TFAB1C009266008食品業者登錄字號:F-111912601-00000-4添...
![](https://i.imgur.com/xOaDO5F.jpg)
【丙酮酸】食品添加物產品登錄碼:TFAB30000233264
添加物名稱:丙酮酸;PyruvicAcid食品添加物產品登錄碼:TFAB30000233264食品業者登錄字號:N-128151176-00000-2添加物分類:型態...
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添加物名稱:乙醯乳酸脫羧酶;MaturexPro(ALDC)食品添加物產品登錄碼:TFAB20000059528食品業者登錄字號:A-114012061-00000-3添...
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【鹽酸硫胺明 (維生素B1,鹽酸色噻胺)】食品添加物產品登錄碼:TFAB1M013025006
添加物名稱:鹽酸硫胺明(維生素B1,鹽酸色噻胺);ThiamineHydrochloride(VitaminB1)食品添加物產品登錄碼:TFAB1M013025006食品...
![](https://i.imgur.com/xOaDO5F.jpg)
【鹽酸硫胺明 (維生素B1,鹽酸色噻胺)】食品添加物產品登錄碼:TFAB1M012856007
添加物名稱:鹽酸硫胺明(維生素B1,鹽酸色噻胺);ThiamineHydrochloride(VitaminB1)食品添加物產品登錄碼:TFAB1M012856007食品...
![](https://i.imgur.com/xOaDO5F.jpg)
【硝酸硫胺明 (維生素B1,硝酸噻胺)】食品添加物產品登錄碼:TFAB1M012857008
添加物名稱:硝酸硫胺明(維生素B1,硝酸噻胺);ThiamineMononitrate(VitaminB1)食品添加物產品登錄碼:TFAB1M012857008食品業者...
![](https://i.imgur.com/xOaDO5F.jpg)
【檸檬香基 K-11-3A-TF】食品添加物產品登錄碼:TFAA30000457991
添加物名稱:檸檬香基K-11-3A-TF;LEMONBASEK-11-3A-TF食品添加物產品登錄碼:TFAA30000457991食品業者登錄字號:H-122868808-00...
![](https://i.imgur.com/xOaDO5F.jpg)
【硝酸硫胺明(維生素B1)】食品添加物產品登錄碼:TFAB1M010346009
添加物名稱:硝酸硫胺明(維生素B1);THIAMINEMONONITRATE食品添加物產品登錄碼:TFAB1M010346009食品業者登錄字號:B-156065601-...
![](https://i.imgur.com/xOaDO5F.jpg)
【硝酸硫胺明(維生素B1)】食品添加物產品登錄碼:TFAB1C009139007
添加物名稱:硝酸硫胺明(維生素B1);THIAMINEMONONITRATE食品添加物產品登錄碼:TFAB1C009139007食品業者登錄字號:A-122443021-...
![](https://i.imgur.com/xOaDO5F.jpg)
【噻唑】食品添加物產品登錄碼:TFAB30000293518
添加物名稱:噻唑;THIAZOLE食品添加物產品登錄碼:TFAB30000293518食品業者登錄字號:A-112298913-00000-3添加物分類:型態:液狀...
![](https://i.imgur.com/xOaDO5F.jpg)
【鹽酸硫胺明 (維生素B1,鹽酸色噻胺)】食品添加物產品登錄碼:TFAB1M012878001
添加物名稱:鹽酸硫胺明(維生素B1,鹽酸色噻胺);ThiamineHydrochloride(VitaminB1)食品添加物產品登錄碼:TFAB1M012878001食品...
![](https://i.imgur.com/xOaDO5F.jpg)
【鹽酸硫胺明(維生素B1)】食品添加物產品登錄碼:TFAB1M011880003
添加物名稱:鹽酸硫胺明(維生素B1);THIAMINEHYDROCHLORIDE(VITAMINB1)食品添加物產品登錄碼:TFAB1M011880003食品業者登錄字號...
![](https://i.imgur.com/xOaDO5F.jpg)
【鹽酸硫胺明(維生素B1)】食品添加物產品登錄碼:TFAB1M012496007
添加物名稱:鹽酸硫胺明(維生素B1);THIAMINEHYDROCHLORIDE(VITAMINB1)食品添加物產品登錄碼:TFAB1M012496007食品業者登錄字號...